Original Article
Sporadic supravalvular stenosis in a young man
Authors:
KM Ghodduci ,
Department of Radiology, UZ Brussel, Brussels, Belgium, BE
M Antic,
Department of Radiology, UZ Brussel, Brussels, Belgium, BE
K Tanaka,
Department of Radiology, UZ Brussel, Brussels, Belgium, BE
D Verdries,
Department of Radiology, UZ Brussel, Brussels, Belgium, BE
D Kerkhove
Department of Department of Cardiology, UZ Brussel, Brussels, Belgium, BE
Abstract
Supravalvar aortic stenosis (SVAS) is a form of congenital left ventricular outflow tract (LVOT) obstruction that occurs as a localized or diffuse narrowing of the ascending aorta beyond the superior margin of the sinuses of Valsalva. SVAS is a rare progressive congenital heart defect with a higher risk of sudden cardiac death. Our patient was a 30-yearold man referred by his GP for an incidental finding of heart murmur. Echocardiography showed a hypertrophic left ventricle with an increased pressure gradient. CT and MRI angiography and eventual arteriography confirmed the diagnosis by showing a narrowing of the aorta at the sinotubular junction with significant accelerated flow. This stenosis was eventually surgically corrected with no complications.
How to Cite:
Ghodduci K, Antic M, Tanaka K, Verdries D, Kerkhove D. Sporadic supravalvular stenosis in a young man. JBR-BTR. 2013;96(1):27–9. DOI: http://doi.org/10.5334/jbr-btr.175
Published on
01 Jan 2013.
Peer Reviewed
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