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Original Article

Sporadic supravalvular stenosis in a young man

Authors:

KM Ghodduci ,

Department of Radiology, UZ Brussel, Brussels, Belgium, BE
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M Antic,

Department of Radiology, UZ Brussel, Brussels, Belgium, BE
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K Tanaka,

Department of Radiology, UZ Brussel, Brussels, Belgium, BE
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D Verdries,

Department of Radiology, UZ Brussel, Brussels, Belgium, BE
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D Kerkhove

Department of Department of Cardiology, UZ Brussel, Brussels, Belgium, BE
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Abstract

Supravalvar aortic stenosis (SVAS) is a form of congenital left ventricular outflow tract (LVOT) obstruction that occurs as a localized or diffuse narrowing of the ascending aorta beyond the superior margin of the sinuses of Valsalva. SVAS is a rare progressive congenital heart defect with a higher risk of sudden cardiac death. Our patient was a 30-yearold man referred by his GP for an incidental finding of heart murmur. Echocardiography showed a hypertrophic left ventricle with an increased pressure gradient. CT and MRI angiography and eventual arteriography confirmed the diagnosis by showing a narrowing of the aorta at the sinotubular junction with significant accelerated flow. This stenosis was eventually surgically corrected with no complications.

How to Cite: Ghodduci K, Antic M, Tanaka K, Verdries D, Kerkhove D. Sporadic supravalvular stenosis in a young man. Journal of the Belgian Society of Radiology. 2013;96(1):27–9. DOI: http://doi.org/10.5334/jbr-btr.175
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Published on 01 Jan 2013.
Peer Reviewed

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